An Isle of Man resident has been diagnosed with CJD.
The Department of Health has confirmed that the person has an extremely rare form of the disease called Sporadic CJD.
It affects one in a million people and this particular strain is not related to beef, cattle or any other animals.
The public health division says the patient is not infectious and there is no risk of transmission.
There are unconfirmed reports that the person involved has died, the Department of Health has so far refused to comment.
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